Vol. 5, Issue 1, Part A (2023)

The Arnold-chiari malformation is a spectrum of congenital malformations of central nervous system characterized by downward displacement of the parts of cerebellum, fourth ventricle, pons and medulla oblongata into the cervical spinal canal. It is one of the commonest causes for congenital hydrocephalus, it is associated with acromesomelic dwarfism for which exact etiology is not known. 
We are reporting a case of primigravida with full term gestation with type 2 Arnoldchiari malformation with CPD in labour. Emergency caesarean section was done. A live male 4.42 kg baby was extracted. Baby died on the 10th day.